Pulmonary Lymphangiomyomatosis in Bourneville’s Tuberous Sclerosis: Case Report

  • Asmae El Ismaili Department of pneumology, UniversityHospital Hassan II, Fes, Morocco
  • Mouni A Serraj Department of pneumology, UniversityHospital Hassan II, Fes, Morocco
  • Bouchra Amara Department of pneumology, UniversityHospital Hassan II, Fes, Morocco
  • M. C. Benjelloun Department of pneumology, UniversityHospital Hassan II, Fes, Morocco
Keywords: Bilateral pneumothorax, Bourneville’s Tuberoussclerosis, Pulmonary lymphangiomyomatosis, Subependymal Cerebral nodules.

Abstract

Lymphangiomyomatosisis a rare disease characterized by a proliferation of abnormal smooth muscle cells responsible for infiltration with the destruction of tissue architecture and genesis of cystic lung and lymphatic lesions. In addition to lung damage, Bourneville’s tuberous sclerosis (BTS) also affects the skin, brain, retina, kidneys, and, less frequently, the heart and bone. We report the case of a young patient with bilateral pneumothorax revealing pulmonary lymphangiomyomatosis in the context of Bourneville’stuberoussclerosis BTS.
Published
2020-05-08
How to Cite
El Ismaili, A., Serraj, M., Amara, B., & Benjelloun, M. (2020). Pulmonary Lymphangiomyomatosis in Bourneville’s Tuberous Sclerosis: Case Report. International Journal of Health and Biological Sciences, 3(02), 06-08. https://doi.org/10.46682/ijhbs.3.2.2